Endomyocardial Fibrosis
Also written as EMF.
| RCM | Sarcomeric mutations, familial amyloidosis | Endomyocardial fibrosis, cardiac tuberculosis, untreated sickle cell disease (iron overload) |
What our notes say
- | RCM | Sarcomeric mutations, familial amyloidosis | Endomyocardial fibrosis, cardiac tuberculosis, untreated sickle cell disease (iron overload) | (Cardiomyopathies)
- Infiltrative & Interstitial: Endomyocardial fibrosis (EMF)—endemic to warm, humid tropical belts—causes apical obliteration and severe restriction via subendocardial fibrous tissue deposition. (Cardiomyopathies)
- | Cardiogenic | Primary pump failure | Rheumatic heart disease, acute coronary syndromes, endomyocardial fibrosis, peripartum cardiomyopathy | (Shock and cardiovascular emergencies)
- Restrictive: normal chamber size, stiff walls, diastolic dysfunction — amyloidosis, sarcoidosis, endomyocardial fibrosis (Cardiovascular & Respiratory Pathology: Atherosclerosis, RHD & MI Review)
- Causes include amyloidosis (most common in the developed world), endomyocardial fibrosis (most common worldwide, particularly in tropical Africa), sarcoidosis, and hemochromatosis. (Heart Pathology: Comprehensive Short Notes)
- Endomyocardial fibrosis — most common worldwide (tropical Africa) (Comprehensive Heart Pathology Notes 🫀)