Restrictive Cardiomyopathy
Also written as RCM.
Look for a prominent *v* wave if functional tricuspid regurgitation is present, or a positive Kussmaul sign (paradoxical rise in JVP on inspiration) typical of restrictive cardiomyopathy (RCM).
Restrictive Cardiomyopathy (RCM)
- Endomyocardial fibrosis, granulomatous deposition, or iron overload $\rightarrow$ Massive accumulation of fibrotic tissue or abnormal proteins within the myocardial interstitium $\rightarrow$ Rigid, non-compliant ventricular myocardium $\ri
Restrictive Cardiomyopathy
- Stiff, non-compliant ventricles → diastolic dysfunction , normal EF
- Amyloidosis — most common in developed world; "sparkling" on echo
- Endomyocardial fibrosis — most common worldwide (tropical Africa)
- Sarcoidosis, hemochromatosis, radiation fibrosis
Read this in Comprehensive Heart Pathology Notes 🫀
What our notes say
- Look for a prominent *v* wave if functional tricuspid regurgitation is present, or a positive Kussmaul sign (paradoxical rise in JVP on inspiration) typical of restrictive cardiomyopathy (RCM). (Cardiomyopathies)
- What is the most likely diagnosis? → Restrictive Cardiomyopathy (RCM) (🫀 MISSING TOPICS — ULTRA DEEP NOTES)
- Restrictive Cardiomyopathy (RCM): Impaired ventricular filling and increased myocardial stiffness with normal or near-normal wall thickness, preserved systolic function, and dilated biatrial chambers. (Cardiomyopathies)
- | Restricted filling | Mitral stenosis, constrictive pericarditis, restrictive cardiomyopathy, hypertrophic cardiomyopathy | (CVS History & Physical Exam: Symptoms, Chest Pain & Syncope)
- *Restrictive cardiomyopathy* — diastolic dysfunction from myocardial infiltration (amyloid, sarcoidosis) (Essential Cardiovascular Pathology: Atherosclerosis to Endoc)
- Organs affected: kidney (nephrotic syndrome), heart (restrictive cardiomyopathy), liver, spleen, nerves (General Pathology Revision: Cell Injury, Inflammation & Adaptation (MBPA 3500 Pa)